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Moderate Chiari I with Syringohydromyelia

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This is an MRI of the brain in an eight-year-old

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female that was performed for headaches.

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And at first glance,

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all the major things that we look for are normal.

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The ventricles are normal in size.

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We're not seeing any mass.

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Now,

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notice you can see some movement artifact on this.

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This is very common in children,

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especially at around the eight-year age.

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Younger than that,

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we often sedate patients.

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Older than that, they can hold still.

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This small amount of motion artifact

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is actually, I think,

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an acceptable amount of artifact that allows

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this child to have an MRI scan

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without needing sedation.

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I think it's worth that we won't miss anything

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if we look carefully at all the sequences.

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Now, as we go inferiorly towards the

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level of the foramen magnum,

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we're seeing the cerebellar tonsils at the level

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of the foramen magnum around the brainstem.

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We're seeing fullness here.

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That's then better characterized

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on this sagittal image.

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On this sagittal image,

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we can see the basion,

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which is the inferior aspect of the basiocciput,

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representing the anterior margin

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of the foramen magnum,

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and we see the opisthion.

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This is also part of the occipital bone that

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represents the posterior margin

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of the foramen magnum.

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If we draw a line between the

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basion and the opisthion,

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we can measure the extent of cerebellar

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tonsillar ectopia.

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In this case,

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the cerebellar tonsils extend

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approximately 13 mm below the plane

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of the foramen magnum.

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But beyond that,

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we're also seeing a contour abnormality in

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the posterior aspect of the spinal cord.

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This is in conjunction with

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a paucity of CSF spaces.

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There is near-complete effacement

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of the CSF space ventral

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to the cervical medullary junction

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at the level of the foramen magnum.

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There's a slightly retroflexed odontoid process,

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and we're seeing effacement of the cisterna magna.

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So, there's a paucity of CSF spaces here.

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So, one of the things commonly that can

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be performed is a CSF flow study

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to look at CSF flow dynamics.

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An additional follow-up study can be

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imaging of the cervical spine.

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You may not have time to do them initially when

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you're first identifying this, but at follow-up,

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you can.

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But beyond those findings,

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we need to look at all the images we have available,

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all the data we have available.

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And if we look in this sagittal image,

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we can actually see here

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syringohydromyelia in the mid-cervical cord.

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This is a CSF collection within the

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central canal of the spinal cord.

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So, even though this is a dedicated brain study,

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we can actually see this abnormality here.

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So, from my perspective, yes, we can,

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at follow-up, perform a CSF flow study,

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but they've already failed.

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The physiologic CSF flow study.

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We already know there's an abnormal CSF flow

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dynamics at the level of the foramen magnum.

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Now,

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spine imaging becomes important to understand

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the caudal extent of this,

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because we're not imaging this

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syringohydromyelia in its entirety.

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So this patient has a Chiari Type I malformation

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with 13 mm of cerebellar tonsillar ectopia.

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But we already know they have

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syringohydromyelia.

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So, this is a patient who likely would not

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benefit from conservative management and may

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require a posterior fossa decompression.

Report

Description

Faculty

Asim F Choudhri, MD

Chief, Pediatric Neuroradiology

Le Bonheur Children's Hospital

Tags

Spine

Pediatrics

Neuroradiology

Musculoskeletal (MSK)

MRI

Idiopathic

Congenital

Brain

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