Interactive Transcript
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I want to finish up the congenital section
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with demonstration of dural ectasia.
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Dural ectasias can occur de novo, or they can be
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associated with a variety of different syndromes.
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By dural ectasia, we're effectively saying that there is
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expansion of the subarachnoid space and expansion
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of the intraspinal dural spaces.
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And this generally leads to posterior
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scalloping of vertebrae.
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So you see that these vertebrae are indented by what
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appears to be the subarachnoid space and the dura.
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This is what was referred to as dural ectasia.
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If we think about a lateral thoracic meningocele, we
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could say that that also is a variety of dural ectasias.
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And dural ectasias are associated with
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neurofibromatosis type 1.
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So in our differential diagnosis of dural ectasia, we have
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neurofibromatosis type 1, which can account for the
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posterior scalloping that you see in this lumbar region,
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and it may also be associated with a lateral thoracic
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meningocele. The other entities are Marfan syndrome.
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The Marfan syndrome, again, is a connective tissue disorder
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which may be associated with a similar variety
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of posterior scalping and dural ectasia.
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We then generally include the mucopolysaccharidoses.
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And the mucopolysaccharidoses may also be associated
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with thickening of the dura at the C1-C2 junction in general
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leading to potentially narrowing also at the foramen magnum.
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So the various types of mucopolysaccharidoses
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are also in the differential diagnoses.
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Patients who have achondroplasia
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also may have dural ectasias.
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And if the patient has a cause of an obstructive
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hydrocephalus intracranially,
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it also may lead to a dural ectasia.
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So there's a variety in the differential diagnoses.
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These are some of the most common and it requires you to
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be looking at other aspects of the imaging in order
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to diagnose these variety of congenital disorders.
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