Upcoming Events
Log In
Pricing
Free Trial

Hemangioblastoma at the Conus Medullaris

HIDE
PrevNext

0:00

This is a young gentleman who presented with

0:03

bowel and bladder incontinence.

0:06

In this case, we have the T1-weighted,

0:08

the T2-weighted scans,

0:10

and I'm going to show the sagittal STIR image as well.

0:14

What one sees is that this looks like a

0:17

predominantly cystic lesion at the conus medullaris,

0:21

which is the termination of the spinal cord.

0:24

So, a cystic lesion in this location could be

0:28

secondary to a distal terminal syrinx,

0:31

or it could be from a cystic neoplasm.

0:34

For this reason,

0:35

the post-gadolinium-enhanced scan is most helpful.

0:39

As we scroll side to side,

0:41

we note that the patient does indeed show a

0:44

contrast enhancing nodule along the posterior

0:46

lateral wall of the cystic mass.

0:50

This cystic mass has all the characteristics

0:52

of an intradural intramedullary lesion,

0:55

in that the CSF space is narrowed at the site of the lesion.

1:00

So how do we know where this cystic

1:02

mass, that has a mural nodule,

1:04

is an ependymoma, an astrocytoma

1:07

or a hemangioblastoma?

1:09

Classically, a lesion that is cystic with a mural nodule of

1:14

enhancement is going to be a hemangioblastoma.

1:18

However, in this case, we have one added feature

1:21

which is important to note.

1:23

If I magnify this sagittal T2-weighted scan

1:29

and drop it down lower,

1:33

we are seeing prominence to the blood vessels

1:37

on the surface of the spinal cord.

1:39

And this is duplicated

1:43

on the post-gadolinium-enhanced scan.

1:47

So as I scroll,

1:48

we see multiple blood vessels on the surface of

1:51

the spinal cord, which are larger

1:53

in size than one would expect.

1:55

And they seem to go down towards that mural nodule.

1:58

That identifies that this is likely a hypervascular mass,

2:03

which is typical of hemangioblastoma.

2:07

Just for completion sake,

2:09

let's look at the axial post-gadolinium

2:11

enhanced sequences.

2:14

And again, we see that the patient has the mural

2:17

nodule on the left side posteriorly,

2:20

the cystic component associated with it,

2:24

and the prominent blood vessels

2:27

superficially along the

2:31

conus medullaris, as well as in the cauda equina

2:35

nerve roots, coursing down the large blood vessels

2:40

posteriorly located.

2:42

So, a classic hemangioblastoma of the spinal cord,

2:47

differential diagnosis with ependymoma and

2:50

astrocytoma being mural nodule associated with a cyst,

2:55

with hypervascularity identified by

2:58

demonstrating large blood vessels leading to the mass.

Report

Description

Faculty

David M Yousem, MD, MBA

Professor of Radiology, Vice Chairman and Associate Dean

Johns Hopkins University

Tags

Spine

Neuroradiology

Neoplastic

Musculoskeletal (MSK)

MRI

© 2024 Medality. All Rights Reserved.

Contact UsTerms of UsePrivacy Policy