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Training Collections
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Practice-focused training programs designed to help you gain experience in a specific subspecialty area.
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Complete all of your state CME requirements in one convenient place.
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Dr. Resnick's MSK Conference
Learn directly from the MSK Master himself.
Lower Extremities MRI Conference
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Supplement your training program with case-based learning for residents, registrars, fellows, and more.
For Private Practices
Upskill in high growth, advanced imaging areas.
Compliance
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Emergency Call Prep
Prepare trainees to be on call for the emergency department with this specialized training series.
22 topics, 1 hr. 12 min.
Introduction to Neurocutaneous Syndromes Part 1 (NF1)
1 m.Chiari Malformation Type 1 in a Patient with NF1
3 m.NF1, With Waxing and Waning Cystic Lesion
5 m.NF1 with Developing Myelin Vacuolization, and Optic Glioma
4 m.NF1 with Suspicious Lesions and Tortuous Optic Nerve
7 m.NF1 with Bilateral Thalamic Lesions and Differential Diagnosis
5 m.Normal Brain MRI in Patients with NF1
5 m.Mild NF1 Phenotype with Sphenoid Wing Dysplasia
4 m.NF1 with High Grade Glioma
3 m.NF1 with Bilateral Optic Nerve Glioma
3 m.Focal Optic Pathway Glioma in NF1
4 m.NF1 with Fusiform Optic Pathway Glioma
3 m.NF1 with Optic Chiasmatic Glioma
3 m.NF1 with Evolution of Optic Nerve Glioma
5 m.NF1 with Optic Pathway Glioma and Moyamoya Disease
6 m.Developing Right Fusiform Optic Glioma
3 m.Glaucoma, an Orbital Manifestation of NF1
3 m.NF1 with a Brain Stem Lesion and Optic Nerve Glioma
4 m.NF1 with Buphthalmos and Orbital Plexiform Neurofibroma
4 m.MRI Appearance of Sphenoid Wing Dysplasia in NF1
2 m.NF1 with Moyamoya Vasculopathy
4 m.Neurocutaneous Syndromes Part 1 (NF1) Summary
2 m.0:01
This is an MRI of the brain and orbits
0:03
in an eleven-year-old child
0:04
with neurofibromatosis type 1.
0:06
We can see areas of myelin vacuolization
0:09
in the globus pallidus bilaterally.
0:15
We can see there's fusiform enlargement of
0:18
the orbital segment of the left optic nerve.
0:21
There's tortuosity.
0:23
We can see there's a focal kinking in
0:27
the anterior orbital segment
0:29
of the left optic nerve.
0:30
Just this redundancy and tortuosity
0:33
and then, a relatively normal caliber
0:35
by the time we get to the orbital
0:37
apex and the optic canal.
0:39
The right optic nerve looks approximately
0:43
normal caliber.
0:44
But there is some tortuosity
0:46
we can see here.
0:48
If we look at this on the coronal image,
0:52
we can see the tortuosity of
0:55
the right optic nerve,
0:57
the left optic nerve,
0:59
we can see the fusiform enlargement
1:02
and then this tortuosity and redundancy,
1:05
because as it gets larger,
1:08
it has to figure out a way
1:09
to fit into the orbit.
1:13
We can see this post-contrast enhancement
1:16
within this fusiform enlargement,
1:20
also seen here on this coronal image.
1:24
So, this is a fusiform optic pathway glioma
1:27
in the orbital segment of the left optic nerve.
1:30
There's additionally tortuosity of the right
1:32
optic nerve without definite visible discrete glioma.
1:38
Now if we zoom in,
1:40
we can see that this glioma is actually
1:42
pushing on the left lateral rectus muscle.
1:47
On the right,
1:48
we can see, between the optic nerve,
1:51
we can see intraconal fat between the optic
1:54
nerve sheath complex and the medial rectus,
1:57
as well as laterally in the lateral
1:59
intraconal space between the optic nerve
2:00
sheath complex and the lateral rectus muscle.
2:04
Here, there is contact with the medial rectus
2:09
muscle and there's actually tenting
2:11
of the lateral rectus muscle.
2:13
It's pushing it outward.
2:15
So, this is an example of a fusiform left
2:19
optic pathway glioma in the setting
2:20
of neurofibromatosis type 1.
Interactive Transcript
0:01
This is an MRI of the brain and orbits
0:03
in an eleven-year-old child
0:04
with neurofibromatosis type 1.
0:06
We can see areas of myelin vacuolization
0:09
in the globus pallidus bilaterally.
0:15
We can see there's fusiform enlargement of
0:18
the orbital segment of the left optic nerve.
0:21
There's tortuosity.
0:23
We can see there's a focal kinking in
0:27
the anterior orbital segment
0:29
of the left optic nerve.
0:30
Just this redundancy and tortuosity
0:33
and then, a relatively normal caliber
0:35
by the time we get to the orbital
0:37
apex and the optic canal.
0:39
The right optic nerve looks approximately
0:43
normal caliber.
0:44
But there is some tortuosity
0:46
we can see here.
0:48
If we look at this on the coronal image,
0:52
we can see the tortuosity of
0:55
the right optic nerve,
0:57
the left optic nerve,
0:59
we can see the fusiform enlargement
1:02
and then this tortuosity and redundancy,
1:05
because as it gets larger,
1:08
it has to figure out a way
1:09
to fit into the orbit.
1:13
We can see this post-contrast enhancement
1:16
within this fusiform enlargement,
1:20
also seen here on this coronal image.
1:24
So, this is a fusiform optic pathway glioma
1:27
in the orbital segment of the left optic nerve.
1:30
There's additionally tortuosity of the right
1:32
optic nerve without definite visible discrete glioma.
1:38
Now if we zoom in,
1:40
we can see that this glioma is actually
1:42
pushing on the left lateral rectus muscle.
1:47
On the right,
1:48
we can see, between the optic nerve,
1:51
we can see intraconal fat between the optic
1:54
nerve sheath complex and the medial rectus,
1:57
as well as laterally in the lateral
1:59
intraconal space between the optic nerve
2:00
sheath complex and the lateral rectus muscle.
2:04
Here, there is contact with the medial rectus
2:09
muscle and there's actually tenting
2:11
of the lateral rectus muscle.
2:13
It's pushing it outward.
2:15
So, this is an example of a fusiform left
2:19
optic pathway glioma in the setting
2:20
of neurofibromatosis type 1.
Report
Description
Faculty
Asim F Choudhri, MD
Chief, Pediatric Neuroradiology
Le Bonheur Children's Hospital
Tags
Syndromes
Pediatrics
Neuroradiology
Neuro
Neoplastic
MRI
Brain
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